Idiopathic Pulmonary Fibrosis (IPF) is a progressive and fatal interstitial lung disease that causes fibrosis in the lungs and is often confused with common diseases such as chronic obstructive pulmonary disease (COPD), asthma, and congestive heart failure (CHF). First-line healthcare professionals play an important role in the early recognition and referral of patients with suspected IPF to a pulmonary specialist. Following are resources to help you recognize the signs and symptoms of IPF.

IPF: What to Look For

IPF is a progressive fatal lung disease often associated with non-specific symptoms

Shortness of breath is the most prominent symptom in IPF and is often progressive

Although nonspecific, cough can be the initial manifestation of ILD

Auscultated “Velcro” crackles are detected in >80% of patients

Raghu G, et al. Am J Respir Crit Care Med. 2011;183:788-824.
Raghu G, Brown K. Clin Chest Med. 2004;25(3):409-419.

IPF: Recognize and Refer

Access the following tools to aid in your recognition and referral

Diagnosing IPF

This video will provide a brief overview to aid a healthcare professional to recognize a potential patient with IPF, encouraging a referral to a pulmonologist if IPF is suspected

IPF Checklist

Access this IPF checklist to aid in recognizing IPF

If you suspect a patient with IPF, refer them to your local pulmonologist or interstitial lung disease (ILD) center for a complete evaluation

The Risk Factors of IPF

A smoking history of more than 20 pack-years is strongly associated with IPF

IPF mainly occurs in patients who are older than 60 years of age

Exposure to metal or wood dust increases the risk of developing IPF

Raghu G, et al. Am J Respir Crit Care Med. 2011;183:788-824.
Baumgartner KB, et al. Am J Epidemiol. 2000;152:307-315.

More Resources for the Healthcare Professional

Download this Special Report authored by experts in interstitial lung disease for in depth information on IPF, as well as the importance of early recognition and referral

Download this Special Report written by Dr. Jonathan Ilowite, of UBM Medica, which provides guidance on the need for healthcare professionals to be aware of IPF, in an effort to encourage faster referrals to pulmonologists

Further information is available by accessing the following websites

(Please click directly on each logo for further information)

IPF education and resources for healthcare professionals

IPF awareness and advocacy

Once an IPF diagnosis is confirmed, this site is for patients and caregivers

Mobilizes people and resources to provide access to high quality care